The LRPPRC antibody from Wuhan Fine Biotech Co., Ltd. is a Rabbit Polyclonal antibody to LRPPRC. This antibody recognizes Homo Sapiens, Human, Mouse, and Rat antigen. The LRPPRC antibody has been validated for the following applications: EIA, Immunoassay, ELISA, Immunohistochemistry, and Western Blot.
Description
This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome